Highlighter is on. Drag to highlight text. Click a highlight to remove it.
ALL / Cardiology
Ebstein's anomaly
Ebstein's anomaly
Ebstein's anomaly is a congenital heart defect characterised by low insertion of the tricuspid valve resulting in a large atrium and small ventricle. It is sometimes referred to as 'atrialisation' of the right ventricle.Ebstein's anomaly may be caused by exposure to lithium in-utero.
Associations
- patent foramen ovale (PFO) or atrial septal defect (ASD) is seen in at least 80% of patients, resulting in a shunt between the right and left atria
- Wolff-Parkinson White syndrome
Clinical features
- cyanosis
- prominent 'a' wave in the distended jugular venous pulse,
- hepatomegaly
- tricuspid regurgitation
- pansystolic murmur, worse on inspiration
- right bundle branch block → widely split S1 and S2
+PassMedicine Notes
Ebstein's anomaly is a congenital heart defect characterised by low insertion of the tricuspid valve resulting in a large atrium and small ventricle. It is sometimes referred to as 'atrialisation' of the right ventricle.
Ebstein's anomaly may be caused by exposure to lithium in-utero.
Associations- patent foramen ovale (PFO) or atrial septal defect (ASD) is seen in at least 80% of patients, resulting in a shunt between the right and left atria
- Wolff-Parkinson White syndrome
- cyanosis
- prominent 'a' wave in the distended jugular venous pulse,
- hepatomegaly
- tricuspid regurgitation
- pansystolic murmur, worse on inspiration
- right bundle branch block --> widely split S1 and S2
